| Source | Code | Name | Case count | Share of cases (%) |
|---|---|---|---|---|
| OUTPAT | OUTPAT_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica | 1029 | |
| INPAT | INPAT_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica | 606 | |
| OUTPAT | OUTPAT_ICD10(M313) | Wegener's granulomatosis | 480 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 366 | |
| INPAT | INPAT_ICD10(M313) | Wegener's granulomatosis | 336 | |
| OUTPAT | OUTPAT_ICD10(M316) | Other giant cell arteritis | 219 | |
| OUTPAT | OUTPAT_ICD10(M319) | Necrotizing vasculopathy, unspecified | 210 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M313) | Wegener's granulomatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 169 | |
| OUTPAT | OUTPAT_ICD10(M317) | Microscopic polyangiitis | 163 | |
| OUTPAT | OUTPAT_ICD10(M311) | Thrombotic microangiopathy | 152 | |
| INPAT | INPAT_ICD10(M319) | Necrotizing vasculopathy, unspecified | 129 | |
| OUTPAT | OUTPAT_ICD10(M310) | Hypersensitivity angiitis | 114 | |
| INPAT | INPAT_ICD10(M316) | Other giant cell arteritis | 113 | |
| OUTPAT | OUTPAT_ICD10(M318) | Other specified necrotizing vasculopathies | 110 | |
| INPAT | INPAT_ICD10(M311) | Thrombotic microangiopathy | 96 | |
| INPAT | INPAT_ICD10(M317) | Microscopic polyangiitis | 96 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M316) | Other giant cell arteritis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 79 | |
| INPAT | INPAT_ICD10(M310) | Hypersensitivity angiitis | 72 | |
| INPAT | INPAT_ICD10(M318) | Other specified necrotizing vasculopathies | 59 | |
| INPAT | INPAT_ICD9(4476A) | Arteritis, unspecified | 55 | |
| OUTPAT | OUTPAT_ICD10(M314) | Aortic arch syndrome [Takayasu] | 55 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M317) | Microscopic polyangiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 33 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M319) | Necrotizing vasculopathy, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 32 | |
| INPAT | INPAT_ICD8(44698) | Polyarteritis nodosa and allied conditions, Other | 31 | |
| INPAT | INPAT_ICD10(M314) | Aortic arch syndrome [Takayasu] | 30 | |
| DEATH | DEATH_ICD10(M313) | Wegener's granulomatosis | 28 | |
| INPAT | INPAT_ICD9(4462A) | Hypersensitivity angiitis | 28 | |
| INPAT | INPAT_ICD9(4465A) | Giant cell arteritis | 26 | |
| INPAT | INPAT_ICD9(4464A) | Wegener's granulomatosis | 23 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M314) | Aortic arch syndrome [Takayasu]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 18 | |
| OUTPAT | OUTPAT_ICD10(M312) | Lethal midline granuloma | 15 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M310) | Hypersensitivity angiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 14 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M318) | Other specified necrotizing vasculopathies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 13 | |
| DEATH | DEATH_ICD10(M317) | Microscopic polyangiitis | 11 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M311) | Thrombotic microangiopathy. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 10 | |
| INPAT | INPAT_ICD9(4466A) | Thrombotic microangiopathy | 8 | |
| INPAT | INPAT_ICD9(4467A) | Takayasu's disease | 7 | |
| INPAT | INPAT_ICD10(M312) | Lethal midline granuloma | 6 | |
| DEATH | DEATH_ICD10(M311) | Thrombotic microangiopathy | 5 | |
| DEATH | DEATH_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica | 5 | |
| DEATH | DEATH_ICD10(M319) | Necrotizing vasculopathy, unspecified | 5 | |
| INPAT | INPAT_ICD8(44620) | Polyarteritis nodosa and allied conditions, Other hypersensitivity angiitis | 5 |