| Source | Code | Name | Case count | Share of cases (%) |
|---|---|---|---|---|
| OUTPAT | OUTPAT_ICD10(Q8500) | Neurofibromatosis, type 1 | 211 | |
| OUTPAT | OUTPAT_ICD10(Q8509) | Unspecified neurofibromatosis | 136 | |
| INPAT | INPAT_ICD10(Q8500) | Neurofibromatosis, type 1 | 104 | |
| OUTPAT | OUTPAT_ICD10(Q851) | Tuberous sclerosis | 69 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q8500) | Neurofibromatosis, type 1. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 63 | |
| OUTPAT | OUTPAT_ICD10(Q8501) | Neurofibromatosis, type 2 | 57 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q850) | Neurofibromatosis (nonmalignant). Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 49 | |
| INPAT | INPAT_ICD10(Q8509) | Unspecified neurofibromatosis | 48 | |
| OUTPAT | OUTPAT_ICD10(Q850) | Neurofibromatosis (nonmalignant) | 46 | |
| INPAT | INPAT_ICD10(Q851) | Tuberous sclerosis | 32 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q8509) | Unspecified neurofibromatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 29 | |
| OUTPAT | OUTPAT_ICD10(Q859) | Phakomatosis, unspecified | 24 | |
| OUTPAT | OUTPAT_ICD10(Q8582) | of Hipple-Lindau syndrome | 23 | |
| INPAT | INPAT_ICD10(Q850) | Neurofibromatosis (nonmalignant) | 22 | |
| INPAT | INPAT_ICD10(Q8501) | Neurofibromatosis, type 2 | 21 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q851) | Tuberous sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 21 | |
| INPAT | INPAT_ICD10(Q8582) | of Hipple-Lindau syndrome | 13 | |
| OUTPAT | OUTPAT_ICD10(Q8580) | Peutz-Jegher syndrome | 13 | |
| OUTPAT | OUTPAT_ICD10(Q8583) | Gardner syndrome | 10 | |
| OUTPAT | OUTPAT_ICD10(Q8588) | Other phakomatoses, not elsewhere classified | 10 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q8501) | Neurofibromatosis, type 2. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 10 | |
| INPAT | INPAT_ICD10(Q859) | Phakomatosis, unspecified | 9 | |
| OUTPAT | OUTPAT_ICD10(Q8581) | Sturge-Weber syndrome | 8 | |
| INPAT | INPAT_ICD10(Q8580) | Peutz-Jegher syndrome | 7 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q8582) | of Hipple-Lindau syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 6 | |
| DEATH | DEATH_ICD10(Q850) | Neurofibromatosis (nonmalignant) | 5 | |
| INPAT | INPAT_ICD10(Q8581) | Sturge-Weber syndrome | 5 |